ABSTRACT
A 36-weeks dysmorphic newborn baby who presented with an antenatal diagnosis of intra-abdominal "cyst" and hydrops foetalis was proven to have a large cystic peritonitis. This was secondary to a large pyloroduodenal perforation, causing hemorrhagic ascites and abdominal wall and pedal edema. The peripheral blood picture was consistent with a myeloproliferative state. It was unclear whether the large perforation was secondary to necrotizing enteropathy seen in acute leukemia
Subject(s)
Humans , Male , Pylorus/pathology , Hydrops Fetalis , Intestinal Perforation , Myeloproliferative Disorders , Prenatal DiagnosisABSTRACT
Hypertrophic pyloric stenosis [HPS] is one of the common surgical emergencies in the newborn, needing surgery in the first few weeks of life. However, its presentation at birth is rare. A full term infant presented with hypertrophic pyloric obstruction at birth and was managed successfully by pyloromyotomy. This case is the first encountered in the department of Pediatric Surgery in the Sultanate of Oman and is reported for its rarity and to alert the pediatrician about the uncommon presentation of the common disease